Behcet's disease and AA-type amyloidosis

Abstract

Behcet's disease (BD) is a multisystem disorder characterized by vasculitis. To our knowledge, 52 patients with ED and amyloidosis have previously been described in the literature. Nephrotic syndrome was the most common type of presentation of amyloidosis in these patients. The prognosis of patients with ED and amyloidosis has not been reported before, in this report, we present a patient with ED and AA-type amyloidosis and analyze the prognosis in these patients, Follow-up and prognosis have been reported in 23 patients. Ten of these 23 patients died and most of these deaths occurred within 3 months after the diagnosis of amyloidosis, Endstage renal disease developed shortly in 4 patients, ED should be considered in the differential diagnosis of AA amyloidosis. In conclusion, the cases with ED and amyloidosis carry poor prognosis. Copyright (C) 2000 S. Karger AG, Basel.